Journal of Disability and Oral Health
- Cover Date:
- March 2011
- Print ISSN:
- 1470-8558
- Vol:
- 12
- Issue:
- 1
Sturge -Weber syndrome: a case report with clinical and radiological features
Sturge Weber syndrome (SWS) is an uncommon, sporadically occurring, frequently progressive neuro-cutaneous syndrome, consisting of congenital hamartomatous malformations, often associated with epilepsy and variable oral manifestations. The port-wine nevus (PWN) is usually the first component of the syndrome, ocular and neurological manifestations like convulsions are among the most characteristic features of disease. Intra orally, the angiomatous lesions may involve the gingiva and buccal mucosa. Radiological investigations are most useful, with conventional radiography, computed tomography and magnetic resonance imaging playing a pivotal role in demonstrating the cerebral changes. This is a report of a case with oral involvement and highlights the importance of imaging in diagnosis and a multidisciplinary approach in treatment of SWS.
Key words: Sturge Weber syndrome, port-wine nevus, oral involvement, imaging modalities, tramline calcifications
- Article Price
- £15.00
- Institution Article Price
- £
- Page Start
- 39
- Page End
- 42
- Authors
- Sujatha S Reddy, Atul Kaushik
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